分子量：Calculated MW: 70kDa/74kDa
Observed MW: 74KDa/50KDa

细胞定位：Peroxisome

稀释方法：WB 1:500 - 1:2000
IHC 1:100 - 1:200
IF 1:50 - 1:200

总结：The protein encoded by this gene is the first enzyme of the fatty acid beta-oxidation pathway, which catalyzes the desaturation of acyl-CoAs to 2-trans-enoyl-CoAs. It donates electrons directly to molecular oxygen, thereby producing hydrogen peroxide. Defects in this gene result in pseudoneonatal adrenoleukodystrophy, a disease that is characterized by accumulation of very long chain fatty acids. Alternatively spliced transcript variants encoding different isoforms have been identified.